- Idiopathic pulmonary haemosiderosis
Name = PAGENAME
DiseasesDB = 29717
ICD9 = ICD9|516.1
OMIM = 178550
Idiopathic pulmonary haemosiderosis is a condition affecting the
lungswhich results in bleeding from tiny alveolar capillaries.
One study indicated an annual incidence of 0.24 case per million.cite journal |author=Kjellman B, Elinder G, Garwicz S, Svan H |title=Idiopathic pulmonary haemosiderosis in Swedish children |journal=Acta Paediatr Scand |volume=73 |issue=5 |pages=584–8 |year=1984 |month=September |pmid=6485774 |doi= |url=]
Idiopathic pulmonary haemosiderosis is an uncommon or rare condition in which bleeding in the lungs causes additional problems especially a collection of
iron(FE) which, in itself causes additional lung damage. Iron is an essential component of a hemoglobinmolecule. This molecule is responsible for transporting Oxygenthrough the blood stream and to the individual cells. Such transport is essential for celluar respiration to occur and for life to continue.
*Idiopathic pulmonary hemosiderosis
*Pulmonary hemosiderosis ("also spelled" Pulmonary haemosiderosis)
*Essential brown induration of lung
*Brown induration of lung
Related or similar conditions
There are many pulmonary problems that may seem to mimic hemosiderosis but do not necessarily include the deposits of iron into the lung. The deposition of iron in the lungs, occurring in the form of
hemosiderin, is the defining characteristic of this illness. These other conditions may occur separately or together with hemosiderosis.:* Pulmonary Fibrosis:*Adult Respiratory Distress Syndrome (ARDS):*Immune Complex Disease:*intra-alveolar bleeding
Idiopathic pulmonary haemosiderosis can occur either as a primary lung disorder or as the sequela to other pulmonary, cardiovascular or immune system disorder.
*PH1 involves PH with circulating anti-GMB antibodies.
*PH2 involves PH with immune complex disease such as
systemic lupus erythematosus, SLE.
*PH3 involves no demonstrable immune system involvement.
Death may occur rapidly with acute, massive pulmonary bleeding or over longer periods as the result of continued pulmonary failure and left heart failure.
* [http://www.emedicine.com/ped/topic970.htm |emedicine.com article]
* [http://rarediseases.about.com/cs/hemosiderosis/a/092103.htm | About.com article]
* [http://health.discovery.com/encyclopedias/illnesses.html?article=3289 | Discovery.com article]
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