Cruveilhier–Baumgarten disease

Cruveilhier-Baumgarten disease or Pégot-Cruveilhier-Baumgarten disease is a rare medical condition in which the umbilical or paraumbilical veins are distended, with an abdominal wall bruit (the Cruveilhier-Baumgarten bruit) and palpable thrill, portal hypertension with splenomegaly, hypersplenism and oesophageal varices, with a normal or small liver.

It was first described by Pégot in 1833, and then by Jean Cruveilhier (1835) and Paul Clemens von Baumgarten (1907).[1]

Armstrong et al. (1942) and Steinburg and Galambos (1967) described two different types of the condition:

  • Cruveilhier-Baumgarten syndrome: liver cirrhosis or portal hypertension is the cause of the distension of the paraumbilical veins (i.e. an acquired condition in which the veins reopen due to high portal pressure).
  • Cruveilhier-Baumgarten disease: the distension of the paraumbilical veins is due to failure of umbilical vein closure, with little or no evidence of liver disease found on liver biopsy (i.e. a congenital patency of the umbilical vein leading to portal hypertension).[1]

External links

Cruveilhier-Baumgarten disease at Who Named It?

References

  1. ^ a b Bisseru B, Patel JS (January 1989). "Cruveilhier-Baumgarten (C-B) disease". Gut 30 (1): 136–7. doi:10.1136/gut.30.1.136. PMC 1378244. PMID 2920918. http://gut.bmj.com/cgi/pmidlookup?view=long&pmid=2920918. Retrieved 2009-03-27. 

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  • Cruveilhier — Jean, French pathologist and anatomist, 1791–1874. See C. fascia, C. fossa, fossa navicularis C., C. joint, C. ligaments, under ligament, C. plexus, C. Baumgarten disease, C. Baumgarten murmur, C. Baumgarten sign, C. Baumgarten syndrome …   Medical dictionary

  • Jean Cruveilhier — (born 1791 in Limoges, France; died 1874 in Sussac) was a French anatomist.He was educated at the University of Paris, where in 1825 he succeeded Pierre Augustin Béclard (1785 1825) as professor of anatomy. In 1836 he relinquished the chair of… …   Wikipedia

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